胎儿脊髓栓系综合征（TCS）是一种比较常见的先天性神经管畸形，可引起胎儿出生后不同程度神经系统和泌尿系统疾病症状。随着人们孕期保健意识的增强及产前影像学诊断技术的发展，由此使产前被诊断为TCS胎儿，或疑诊为TCS胎儿呈逐年增多趋势。目前关于胎儿TCS的孕期诊断及围产期管理的文献报道极其少见。孕期一旦被诊断为TCS胎儿，需要多学科团队（MDT）共同评估该病胎儿预后，做出细致产前临床咨询，针对胎儿TCS的不同病因，对TCS胎儿提供个体化围产期处理方案。笔者拟就胎儿TCS的病因、发病机制及分型与合并其他畸形情况，以及产前诊断、围产期处理、结局及预后等的最新研究现状进行阐述，旨在为TCS胎儿的相关临床咨询提供参考和建议。

Fetal tethered cord syndrome（TCS）is a common congenital neural tube malformation that causes neurological and urinary symptoms with varying d egrees after birth.With the increase of people's awareness of health care during pregnancy and rapid development of prenatal imaging t echnology，the prenatal diagnosis of fetal TCS or suspected fetal TCS are gradually increasing.However，there are very few literature reports on the perinatal diagnosis and management of fetal TCS.Once fetal TCS is diagnosed during pregnancy，a multi-disciplinary team（MDT）is required to jointly evaluate the fetal prognosis，make detailed prenatal clinical consultations，and provide individual protocols for TCS fetuses according to different pathogenesis of fetal TCS.This paper intends to focus on the the latest research progress on etiology，pathogenesis，classification and combined other malformations，as well as prenatal diagnosis and management，outcome and prognosis of TCS fetuses，in order to provide reference and suggestions for clinical consultation on TCS fetuses.